[{"@context":"https:\/\/schema.org\/","@type":"Article","@id":"https:\/\/www.lipt.sk\/svalove-poruchy-u-deti\/#Article","mainEntityOfPage":"https:\/\/www.lipt.sk\/svalove-poruchy-u-deti\/","headline":"Svalov\u00e9 poruchy u det\u00ed","name":"Svalov\u00e9 poruchy u det\u00ed","description":"Z\u00edskan\u00e9 svalov\u00e9 ochorenia m\u00f4\u017eu by\u0165 z\u00e1palov\u00e9, infek\u010dn\u00e9, lie\u010div\u00e9, toxick\u00e9. Z\u00e1palov\u00e9 ochorenia \u013eudsk\u00e9ho svalu &#8211; polymyozit\u00edda, dermatopolimiozit\u00edda, myozit\u00edda s inkl\u00faziami, sarkoidn\u00e1 myopatia. Infek\u010dn\u00e1 myozit\u00edda m\u00f4\u017ee by\u0165 v\u00edrusov\u00e1, bakteri\u00e1lna, parazitick\u00e1, at\u010f. Hlavn\u00e9 ","datePublished":"2018-09-09","dateModified":"2018-09-09","author":{"@type":"Person","@id":"https:\/\/www.lipt.sk\/author\/#Person","name":"","url":"https:\/\/www.lipt.sk\/author\/","identifier":1,"image":{"@type":"ImageObject","@id":"https:\/\/secure.gravatar.com\/avatar\/c36ac855b1ee9cce96e09824fb5426d6eaccd04233fbf51e04e067ccd1b5fe13?s=96&d=mm&r=g","url":"https:\/\/secure.gravatar.com\/avatar\/c36ac855b1ee9cce96e09824fb5426d6eaccd04233fbf51e04e067ccd1b5fe13?s=96&d=mm&r=g","height":96,"width":96}},"publisher":{"@type":"Organization","name":"lipt.sk","logo":{"@type":"ImageObject","@id":"\/logo.png","url":"\/logo.png","width":600,"height":60}},"image":{"@type":"ImageObject","@id":"https:\/\/www.lipt.sk\/wp-content\/uploads\/img_a293087_w2015_t1541782073.jpg","url":"https:\/\/www.lipt.sk\/wp-content\/uploads\/img_a293087_w2015_t1541782073.jpg","height":0,"width":0},"url":"https:\/\/www.lipt.sk\/svalove-poruchy-u-deti\/","wordCount":342,"articleBody":"Z\u00edskan\u00e9 svalov\u00e9 ochorenia m\u00f4\u017eu by\u0165 z\u00e1palov\u00e9, infek\u010dn\u00e9, lie\u010div\u00e9, toxick\u00e9. Z\u00e1palov\u00e9 ochorenia \u013eudsk\u00e9ho svalu &#8211; polymyozit\u00edda, dermatopolimiozit\u00edda, myozit\u00edda s inkl\u00faziami, sarkoidn\u00e1 myopatia.Infek\u010dn\u00e1 myozit\u00edda m\u00f4\u017ee by\u0165 v\u00edrusov\u00e1, bakteri\u00e1lna, parazitick\u00e1, at\u010f. Hlavn\u00e9 pr\u00edznaky &#8211; svalov\u00e1 slabos\u0165 a boles\u0165 &#8211; sa objavuj\u00fa ak\u00fatne. Niekedy m\u00f4\u017eu by\u0165 sprev\u00e1dzan\u00e9 ko\u017en\u00fdmi l\u00e9ziami (dermatopolimiozit\u00edda). Charakteristick\u00fdm znakom priebehu t\u00fdchto ochoren\u00ed je zv\u00fd\u0161enie telesnej teploty.Vroden\u00e9 myopatie u det\u00edNeuromuskul\u00e1rne ochorenia m\u00f4\u017eu by\u0165 dedi\u010dn\u00e9, autoimunitn\u00e9 a mytochondri\u00e1lne.1. Myot\u00f3nia Thomsen je zdeden\u00e1, prejavuje sa v ranom detstve. Prv\u00fdm znakom je poru\u0161enie preh\u013atania (spomalenie preh\u013atania, \u010dast\u00e9 vracanie), \u010do je d\u00f4sledkom vysok\u00e9ho t\u00f3nu svalov hrdla. V priebehu \u010dasu, neschopnos\u0165 oddeli\u0165 zovret\u00e9 prstov.2. Pri svalov\u00fdch dystrofi\u00e1ch s\u00fa postihnut\u00e9 samotn\u00e9 svalov\u00e9 vl\u00e1kna. Svalov\u00e1 slabos\u0165 u die\u0165a\u0165a m\u00e1 nasleduj\u00face pr\u00edznaky:\t\tsvalov\u00e1 slabos\u0165;\t\tzn\u00ed\u017een\u00fd svalov\u00fd tonus;\t\toneskorenie det\u00ed v rozvoji motorov;\t\tsvalov\u00e1 atrofia;\t\tskelet\u00e1lne deformity.3. Amyotrofie ovplyv\u0148uj\u00fa nervov\u00e9 vl\u00e1kna miechy alebo samotn\u00e9 nervy. U\u017e od narodenia m\u00f4\u017ee by\u0165 vidie\u0165 u die\u0165a\u0165a:\t\tLetargia\t\tspomalenie v\u00fdvoja\t\tzv\u00fd\u0161enie svalov\u00e9ho objemuDiagn\u00f3za a lie\u010dba svalov\u00fdch chor\u00f4bLie\u010dba neuromuskul\u00e1rnych ochoren\u00ed z\u00e1vis\u00ed od kompetentnej diagn\u00f3zy. M\u00f4\u017ee to by\u0165 lek\u00e1rska, fyzioterapia, terapia vitam\u00ednmi, cvi\u010debn\u00e1 terapia at\u010f. Pri v\u00fdvoji k\u013abovej kontrakt\u00fary a chrbticovej deformity sa aplikuje ortopedick\u00e1 korekcia. Integrovan\u00fd pr\u00edstup k lie\u010dbe det\u00ed so svalovou slabos\u0165ou inhibuje progresiu ochorenia.Na lie\u010dbu neuromuskul\u00e1rnych ochoren\u00ed sa lieky pou\u017e\u00edvaj\u00fa na zlep\u0161enie metabolizmu nervov\u00e9ho tkaniva svalov, anabolick\u00fdch steroidov, l\u00e1tok, ktor\u00e9 zlep\u0161uj\u00fa neuro muskul\u00e1rne vedenie at\u010f. Prevencia ochoren\u00ed svalov u nenaroden\u00e9ho die\u0165a\u0165a sa vykon\u00e1va po\u010das lek\u00e1rsko-genetick\u00e9ho poradenstva rodi\u010dov v \u0161t\u00e1diu pl\u00e1novan\u00e9ho rodi\u010dovstva. Takto s\u00fa odhadovan\u00e9 rizik\u00e1 v\u00fdvoja dedi\u010dn\u00fdch ochoren\u00ed, vr\u00e1tane svalovej patol\u00f3gie.                                                                                                                                                                                                                                                                                                                                                                                        4.1\/5 - (7 votes)        "},{"@context":"https:\/\/schema.org\/","@type":"BreadcrumbList","itemListElement":[{"@type":"ListItem","position":1,"name":"Svalov\u00e9 poruchy u det\u00ed","item":"https:\/\/www.lipt.sk\/svalove-poruchy-u-deti\/#breadcrumbitem"}]}]